Learn. Share. Grow.

Title: Results of growth-friendly management of early-onset scoliosis in children with and without skeletal dysplasias: a matched comparison.

Authors: Helenius IJ, Saarinen AJ, White KK, McClung A, Yazici M, Garg S, Thompson GH, Johnston CE, Pahys JM, Vitale MG, Akbarnia BA, Sponseller PD.

Journal: The Bone and Joint Journal

Date: December 01, 2019

Excerpt: Compared to children with idiopathic EOS, a similar degree of correction of deformity was achieved in children with skeletal dysplasia, but these children gained significantly less spinal growth.

Keywords: Growth friendly, Early onset scoliosis, Skeletal Dysplasia

Summary:

 What is the purpose of this study?

Skeletal dysplasias are a group of varying disorders that involve complicated bone deformities and limited growth that are hard to care for. Many of these patients have less quality of life, made worse with repetitive surgeries. This study explored the outcomes of surgical treatment and quality of life in these children compared to those with idiopathic scoliosis.

Results:

- Patients with skeletal dysplasia and surgery before age ten were compared with patients with idiopathic scoliosis and surgery before age ten.

- Skeletal dysplasia patients were shorter, but the scoliosis curve averages were similar.

Children with skeletal dysplasia had a greater risk of neuromonitoring complications during surgery.

- Quality of life questionnaires showed much lower satisfaction in the dysplasia group of patients than the idiopathic group of patients following surgery.

Important Discussion Points

- Dysplasia patients had similar curve correction, but much less growth than the idiopathic patients.

- The benefit of surgery in patients with skeletal dysplasia is uncertain.

- There are many limitations to our study. Some being: questionnaires not available in all patients and limited pulmonary information.

- It would be wise for a study to compare early fusion skeletal dysplasia patients to these growth friendly surgery patients in deciding best care options.